Hepatic Vascular Variants in Hereditary Haemorrhagic Telangiectasia: Imaging findings

Abstract

Hereditary haemorrhagic telangiectasia (HHT) is an autosomal dominant disorder characterised by vascular dysplasia. Hepatic vascular m alformations (VMs) range from small telangiectases to significant vascular shunting. Here we report two cases of HHT. Case 1 had diffuse ectasia of the hepatic artery along its intrahepatic and extrahepatic course with a hepatic arterial aneurysm. Case 2 presented with ileal and hepatic telangiectases. Knowledge of these vascular variants is indispensable for clinicians and radiologists in aiding diagnosis and surgical and interventional management.

Keywords: Vascular Malformations; Hereditary Haemorrhagic Telangiectasia; Arteriovenous Malformation; Osler Weber Rendu.