Main Article Content
Abstract
Hereditary angioedema (HAE) is a rare disorder caused by a deficiency of C1 esterase inhibitor. Minor trauma and emotional stress are the most common initiating events leading to contact system activation and excessive uncontrolled bradykinin release. This manifests as angioedema, a vascular reaction of the deeper layers of the skin and mucous membranes, with vasodilatation and increased permeability resulting in tissue swelling. Severe angioedema can occur in the perioperative period, leading to fatal airway obstruction. We describe the anaesthetic management of a child with HAE for dental rehabilitation and provide an review of the relevant literature.
Keywords
Anesthesia
Hereditary angioedema
C1 esterase inhibitor deficiency
Case Report
Oman.
Article Details
How to Cite
Narayanan, A., Date, R. R., Birur, S., Bhakta, P., & Srinivasan, S. (2013). Anaesthesia Management of a Patient with Hereditary Angioedema with Prophylactic Administration of C1 Esterase Inhibitor : Case report and literature review. Sultan Qaboos University Medical Journal, 13(3), 467–471. Retrieved from https://journals.squ.edu.om/index.php/squmj/article/view/1852